گزارش یک مورد سندرم آلبرایت

Mccune Albright syndrome is a polyosteotic fibrous dysplasia which manifests itself with disturbance of endocrine function and pigmented patch in skin at birth. The prevalence of polyosteotic is between two and three per million. The upper end of femur is the frequent site of involvement in polyosteotic form with multi endocrinopathy and limb deformity and multiple fractures. The present study is the case report of a 19-year-old girl who referred for left lower limb shortening and deformity of thigh following conservative management. In follow-up, and at the age of 19 due to recurrence of deformity and lower limb shortening(10 cm) the patient underwent derotational subtrochantric valgus osteotomy and bone graft, fixation with plate and concomitant distal femural supracondylar close wedge osteotomy. After operation limb deformity and discrepancy were corrected.